A: There are reasons why someone could have PH. Idiopathic pulmonary arterial hypertension (IPAH) means that there is no known reason for the PH diagnosis. IPAH is rare, occurring in only 2 in one million persons per year.
Secondary PH means that there is an underlying cause for the PH diagnosis. Congenital heart diseases, pulmonary thromboembolism, inflammatory diseases (such as scleroderma, CREST syndrome, or systemic lupus), HIV infections, liver disease, and diet drugs (such as fen-fen) are several reasons for a secondary PH diagnosis. SOMETIMES, but not all the time, the treated underlying condition MAY cure the PH. However, this does not always happen. Managing PH and the cause for it has made living with PH for much longer a bigger possibility nowadays!