1. slowly progressive, lifespan of 20 + years 2. check oromotor apraxia "Lick your lips" "pa-ta-ka, pa-ta-ka" 3. Otherwise normal neuropsych 4. +/- Pet may show left insular/perisylvian abnormality 5. young age 40-80 6. tauopathy like PSP or CBD 7. up-down reversals 8. normal MRI
2. check oromotor apraxia "Lick your lips" "pa-ta-ka, pa-ta-ka"
3. Otherwise normal neuropsych
4. +/- Pet may show left insular/perisylvian abnormality
5. young age 40-80
6. tauopathy like PSP or CBD
7. up-down reversals
8. normal MRI